A difficult airway approach in a merosin-deficient congenital muscular dystrophy patient: a case report

Autor: Jorge Pelicano Paulos, Vanessa Artilheiro, Catarina Cruz, Ana Pinto Carneiro
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Brazilian Journal of Anesthesiology, Vol 73, Iss 5, Pp 683-685 (2023)
Druh dokumentu: article
ISSN: 0104-0014
DOI: 10.1016/j.bjane.2021.03.018
Popis: Merosin-deficient muscular dystrophy is caused by an autosomal recessive mutation on laminin-..2 gene characterized by severe progressive muscle weakness associated with neuromuscular scoliosis and restrictive lung disease. In this case report, we describe an alternative airway approach performed in a child with anticipated difficult airway and merosin-deficient muscular dystrophy. Significant anesthetic implications may increase the perioperative risk, requiring accurate knowledge to anticipate an adequate management and provide patient-safety strategies.
Databáze: Directory of Open Access Journals