RESULTS OF SURGICAL TREATMENT IN THE CRANIOCERVICAL JUNCTION IN MUCOPOLYSACCHARIDOSIS

Autor: Luís Eduardo Carelli Teixeira da Silva, Alderico Girão Campos de Barros, Lucas Rocha Cavalcanti, Caique Jauhar de Castro, Renato Henriques Tavares, Raphael Teofilo de Souza
Jazyk: English<br />Spanish; Castilian<br />Portuguese
Rok vydání: 2016
Předmět:
Zdroj: Coluna/Columna, Vol 15, Iss 1, Pp 57-60 (2016)
Druh dokumentu: article
ISSN: 2177-014X
1808-1851
DOI: 10.1590/S1808-185120161501153519
Popis: ABSTRACT Objective: Evaluate the results after decompression and stabilization of craniocervical junction in patients with mucopolysaccharidosis (MPS). Method: Retrospective study of 10 patients with MPS through the analysis of medical records and additional tests. Result: All patients with mid-term and long-term follow-up achieved consolidation of the arthrodesis and 87.5% had neurological improvement of Nurick score. Conclusion: Early diagnosis and intervention in cases of stenosis and/or craniocervical instability of patients with MPS provide patients a good recovery of neurological function, despite the great technical difficulty and risk of complications.
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