A rare case of hypereosinophilic syndrome presenting with unilateral proptosis and torticollis

Autor: Jayanta K Das, Krati Gupta, Saurabh Deshmukh, Richa Shrivastava
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Indian Journal of Ophthalmology, Vol 66, Iss 10, Pp 1508-1511 (2018)
Druh dokumentu: article
ISSN: 0301-4738
1998-3689
DOI: 10.4103/ijo.IJO_316_18
Popis: Hypereosinophilic syndrome (HES) is a spectrum of myeloproliferative disorder, which is characterized by persistent and marked blood eosinophilia and damage to multiple organs due to eosinophilic infiltration. Idiopathic HES is identified after ruling out all other causes of eosinophilia. Poor prognosis is usually associated with cardiac involvement and malignant transformation of blood cells. We report a rare case of HES in an 8-year-old boy who presented with unilateral proptosis and torticollis. The patient responded well to corticosteroid therapy with reduction of proptosis and torticollis and normalization of serum eosinophil count.
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