| Autor: |
Ryuichi Hoshi, Paula Marcella Silva Drago, Henrique Mascarenhas Villela, Gabriela Gayer Sheibler, Daniel Serra Cassano, Fernanda Barros Silva de Pedreira Barbosa, Lissa Hoshi, Isadora dos Santos Lima |
| Jazyk: |
angličtina |
| Rok vydání: |
2024 |
| Předmět: |
|
| Zdroj: |
Oral and Maxillofacial Surgery Cases, Vol 10, Iss 1, Pp 100340- (2024) |
| Druh dokumentu: |
article |
| ISSN: |
2214-5419 |
| DOI: |
10.1016/j.omsc.2023.100340 |
| Popis: |
Richieri-Costa-Pereira syndrome (RCPS) is a rare genetic disease with an autosomal recessive inheritance pattern characterized by craniofacial alterations such as microsomia, Pierre-Robin sequence, mandibular cleft, absence of lower central incisors, short stature, and changes in the upper and lower limbs. Mandibular clefts are rare and can vary from a slight notch in the lower lip or mandibular alveolus to a complete mandibular cleavage. Only three cases of total mandibular rehabilitation with a customized prosthesis have been published, and none have described a patient born with a mandibular cleft. With the aid of computer-aided design/computer-aided manufacturing technology, virtual surgical planning, and customized manufacturing of surgical materials, the rehabilitation of this case became attainable. In this study, we describe the case of a patient with RCPS and median mandibular cleft treated with a customized total mandibular prosthesis. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
|
