Recurring fibrous dysplasia of anthro maxillary with cranial base invasion

Autor: Sousa, Kátia Maria Marabuco de, Costa, Kárlos Jader Sátiro de Mendonça, Holanda, Thiago Ayres, Silva, Thiago Oliveira e, Cunha, Rafael Levi Louchar Silva da, Soares, Vítor Yamashiro Rocha
Jazyk: angličtina
Rok vydání: 2009
Předmět:
Zdroj: International Archives of Otorhinolaryngology, Vol 13, Iss 3, Pp 331-335 (2009)
Druh dokumentu: article
ISSN: 1809-9777
1809-4864
Popis: Introduction: Fibrous dysplasia is an osseous lesion with an unknown etiology. It is characterized by the osseous maturation insufficiency. It may affect any bone, but the affection of craniofacial bones is the most critical for otorhinolaryngology. Maxilla is the most affected facial bone and the orbitary invasion is an uncommon event. The symptoms are unspecific and for its low suspicion and uncommonness, the diagnosis is generally late. The monostotic form presents a slow growth and asymptomatic course and needs to be followed up. The polyostotic type has a progressive behavior and is associated to recurrence and complications. Objective: To present two cases of patients with fibrous dysplasia diagnosis and describe the clinical presentation, radiological findings and the treatment of this pathology. Cases Report: Two cases of fibrous dysplasia are reported, which initially presented unspecific symptomatology, but with characteristic radiologic signs. They were submitted to surgical treatment for resection of the lesions and evolved with frequent recurrences with extensive affection of the facial sinuses, one patient had cranial base invasion and frontal craniotomy was needed for tumoral excision. Final Comments: Fibrous dysplasia is an uncommon osteopathy. The tomography is the choice method for characterization of the tumoral expansion, and helps in the surgical planning. The surgical strategy is indicated for symptomatic lesions, functions alterations or anatomic disorders. This article describes two uncommon manifestations of recurrent fibrous dysplasia with an extensive affection of anthro maxillary, ethmoidal and sphenoid sinuses, in addition to orbitary and cranial base invasion.
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