Development of acquired intrapulmonary venous anastomosis contributing to establishment of Fontan circulation

Autor: Yasunobu Hayabuchi, Yukako Homma, Mikio Sugano, Takashi Kitaichi, Shoji Kagami
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Pulmonary Circulation, Vol 9 (2018)
Druh dokumentu: article
ISSN: 2045-8940
20458940
DOI: 10.1177/2045894018814774
Popis: Pulmonary venous (PV) obstruction is associated with a poor prognosis, as well as a high risk of recurrence, following surgical treatment. It can also interfere with the successful completion of Fontan circulation in patients with complex congenital heart disease. A case of a patient who had right isomerism (also known as asplenia syndrome), total anomalous pulmonary venous connection (TAPVC), and a single right ventricle is presented. Although bilateral total occlusion of the inferior PVs was identified postoperatively, the formation of the anastomosis and collateral vessels into the superior and middle PVs enabled successful completion of Fontan circulation. Anastomoses and collateral flow of the PVs were found largely in the interlobar pleura and not in the lung parenchyma.
Databáze: Directory of Open Access Journals