Autor: |
Gladys Alejandra Paguaga, Orlando Rodas Pernillo, Helga María Sarti |
Jazyk: |
English<br />Spanish; Castilian<br />French<br />Polish |
Rok vydání: |
2014 |
Předmět: |
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Zdroj: |
Nasza Dermatologia Online, Vol 5, Iss 4, Pp 401-407 (2014) |
Druh dokumentu: |
article |
ISSN: |
2081-9390 |
DOI: |
10.7241/ourd.20144.73 |
Popis: |
Lymphomatoid papulosis (LyP) is an indolent form of primary cutaneous T-cell lymphoma, currently classified together with primary cutaneous anaplastic large T-cell lymphoma within the spectrum of CD30-positive lymphoproliferative disorders. It is characterized by presenting as a clinically benign but histopathological malignant disease. Clinical features consist in recurrent waxing and waning red papules. Histopathologically, there are 4 variants recognized, Type A or Hystiocitic type, being the most frecuent of all, Type B or Mycosis fungoides-like, Type C or Anaplastic large-cell lymphoma-like and Type D, the most recently described and uncommon variant with features similar to Cutaneous Aggressive CD8-Positive Cytotoxic T-Cell Lymphoma. We present a case of a 22-year-old female with multiple papules and nodules in trunk and limbs that after histopathological and immunochemical examination was compatible with Type D LyP. It is important to report this case, as a perfect example of an uncommon variant of LyP, with emphasis in its typical clinical, histopathological and inmunohistochemical findings and review of the literature. |
Databáze: |
Directory of Open Access Journals |
Externí odkaz: |
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