It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation

Autor:	Fayza Haider, Khulood Al Saad, Fatima Al-Hashimi, Hakima Al-Hashimi
Jazyk:	angličtina
Rok vydání:	2017
Předmět:	pleuropulmonary blastoma lung benign or congenital lesions airway (includes related subject matter) infant pediatric Surgery RD1-811
Zdroj:	The Thoracic & Cardiovascular Surgeon Reports, Vol 06, Iss 01, Pp e10-e14 (2017)
Druh dokumentu:	article
ISSN:	2194-7635 2194-7643
DOI:	10.1055/s-0037-1598625
Popis:	Abstract Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are usually advanced with a poor prognosis. We report this case to increase awareness about this entity so that the pediatricians, pediatric surgeons, radiologist, and pathologist recognize it early.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/25feeded195a4246bf5fac14b67052f8 Zobrazit plný text záznamu View record in DOAJ