Oral Rehabilitation as Part of a Multidisciplinary Treatment in a Case Study of Pigmentary Incontinence

Autor: Mónica Cano-Rosás, Joaquín de Vicente-Jiménez, José María Diosdado-Cano, David Suárez-Quintanilla, Rogelio González-Sarmiento, Daniel Curto, Adrián Curto
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Children, Vol 10, Iss 9, p 1505 (2023)
Druh dokumentu: article
ISSN: 10091505
2227-9067
DOI: 10.3390/children10091505
Popis: We present the clinical course of a 9-year-old female patient with Bloch–Sulzberger syndrome and severe neurological deficit that met the major (classic cutaneous signs) and minor (dental anomalies and retinal pathology) diagnostic criteria of Landy and Donnai. Longitudinal multidisciplinary follow-up was carried out from birth to adulthood. Neurological involvement was assessed with electroencephalographic (EEG) and neuroimaging tests at different times during the patient’s life. Cranio-maxillofacial involvement was evaluated using lateral skeletal facial and cephalometric analyses. The right and left facial widths were measured through frontal face analysis and using the vertical zygomatic–midline distance. Oral rehabilitation was performed through orthodontic treatment and major dental reconstruction using composite resins. This treatment aimed to improve the occlusion and masticatory function, relieve the transversal compression of the maxilla, and reconstruct the fractured teeth. We believe that, due to significant neurological and cognitive impairment, orthognathic surgery was not the best option for restoring function and improving oral health-related quality of life.
Databáze: Directory of Open Access Journals