Duodenal biopsy: an unexpected confirmatory test for a patient with al-amyloidosis

Autor: S. Pirasath, T. Kumanan, G. Selvaratnam, V. Sujanitha, D. D. Dikowita
Jazyk: angličtina
Rok vydání: 2019
Předmět:
Zdroj: Sri Lanka Journal of Medicine, Vol 28, Iss 1, Pp 65-69 (2019)
Druh dokumentu: article
ISSN: 2579-1990
DOI: 10.4038/sljm.v28i1.101
Popis: SSystemic AL- amyloidosis is a disorder of protein folding in which there is extra-cellular accumulation as β pleated fibrillar deposits of monoclonal immunoglobulin light chain fragments. AL- amyloidosis is a rare clinical entity. A presentation with clinical and histological evidence of gastrointestinal amyloidosis is even rare. Here we report primary AL- amyloidosis secondary to lamda (λ) light chain myeloma in a middle-aged woman who presented with nephrotic syndrome and motor peripheral neuropathy.
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