Severe Aortic Valvular Incompetence From IgG4-Related Disease

Autor: Bing Wei Thaddeus Soh, MB, Sophie Catherine Prendergast, MB, Louise Burke, MD, Cormac T. O’Connor, MB, Ihsan Ullah, MBBS, Julie M. O’Brien, MB, John A. Hinchion, MB, Samer Arnous, MD, Thomas J. Kiernan, MD
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: JACC: Case Reports, Vol 24, Iss , Pp 102027- (2023)
Druh dokumentu: article
ISSN: 2666-0849
DOI: 10.1016/j.jaccas.2023.102027
Popis: IgG4-related disease (IgG4-RD) is a new clinical entity characterized by lymphoplasmacytic lesions rich in IgG4-positive plasma cells. Myocardial involvement is extremely rare and not a typical cardiovascular manifestation of IgG4-RD. We report a rare case of IgG4-RD–associated myocardial mass causing severe aortic incompetence, successfully treated with surgery and corticosteroids. (Level of Difficulty: Intermediate.)
Databáze: Directory of Open Access Journals