A rare clinical case of pulmonary artery sarcoma

Autor: G. R. Bikbaeva, A. N. Kovalskaya, A. P. Rodin, G. V. Salamov, T. V. Pavlova, D. V. Duplyakov
Jazyk: English<br />Russian
Rok vydání: 2024
Předmět:
Zdroj: Рациональная фармакотерапия в кардиологии, Vol 20, Iss 1, Pp 52-56 (2024)
Druh dokumentu: article
ISSN: 1819-6446
2225-3653
DOI: 10.20996/1819-6446-2024-2984
Popis: Pulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echocardiography revealed a mass in the left pulmonary artery (PA) with obstruction. CT-angiopulmonography showed a filling defect in the left PA, blocking the lumen of the artery by 90%. According to histopathology, the patient was diagnosed with pulmonary artery sarcoma. Subsequently, the following was performed: thrombendarterectomy from the pulmonary artery, combined pneumonectomy on the left side, suturing of the secondary atrial septal defect, followed by 3 courses of monochemotherapy with paclitaxel. After 1 year and 9 months, due to disease progression the patient died. The prognosis of PAS depends on early diagnosis, so doctors should be aware of this disease and use the best treatment options.
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