Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life

Autor: Camila Vieira Bellettini, Rafaela Wagner, Aleocídio Sette Balzanelo, André Luis de Souza Andretta, Arthur Nascimento de Moura, Catia Carolina Fabris, Eduardo Maranhão Gubert
Jazyk: English<br />Spanish; Castilian<br />Portuguese
Předmět:
Zdroj: Revista Paulista de Pediatria, Vol 34, Iss 3, Pp 384-387
Druh dokumentu: article
ISSN: 1984-0462
DOI: 10.1016/j.rppede.2016.03.016
Popis: Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.
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