Biliary atresia and situs inversus in infant: a rare case report

Autor: Rendi Aji Prihaningtyas, Seruni, Bagus Setyoboedi, Sjamsul Arief
Jazyk: angličtina
Rok vydání: 2024
Předmět:
Zdroj: Romanian Journal of Pediatrics, Vol 73, Iss 3, Pp 175-179 (2024)
Druh dokumentu: article
ISSN: 1454-0398
2069-6175
DOI: 10.37897/RJP.2024.3.5
Popis: Background. Biliary atresia is the leading cause of liver transplantation in children. It is associated with other congenital anomalies. The presentation of biliary atresia with situs inversus is a rare case. Case presentation. A 2-month-old female presented with jaundice since 15 days of life, acolic stools, and tea-colored urine. On further evaluation, she was found to have dextrocardia and situs inversus. A liver biopsy was performed and showed hepatic fibrosis due to extrahepatic cholestasis. Abdominal ultrasound and MRCP confirmed a liver in the left hypochondrium and suggested biliary atresia. Conclusion. Although rare, every patient with biliary atresia should be screened for congenital situs inversus, which has a poor prognosis.
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