Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis

Autor: Yen Shen Wong, Zakhirati Zainol Abidin, Aisya Natasya Musa, Roqiah Fatmawati Abdul Kadir, Bushra Johari
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Respiratory Medicine Case Reports, Vol 43, Iss , Pp 101834- (2023)
Druh dokumentu: article
ISSN: 2213-0071
DOI: 10.1016/j.rmcr.2023.101834
Popis: Introduction: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. Case: A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. Conclusion: Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings.
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