Heterotaxy polysplenia syndrome in an adult female with complete endocardial cushion defect

Autor: Habib Ahmad Esmat, Mohammad Wali Naseri, Asadullah Shirzai
Jazyk: angličtina
Rok vydání: 2021
Předmět:
Zdroj: Radiology Case Reports, Vol 16, Iss 5, Pp 1080-1084 (2021)
Druh dokumentu: article
ISSN: 1930-0433
DOI: 10.1016/j.radcr.2021.02.015
Popis: Heterotaxy syndrome is a rare condition characterized by the abnormal arrangement of thoracoabdominal organs across the left-right axis of the body.It is generally classified as right and left atrial isomerism or asplenia and polysplenia syndrome, even though there are overlaps and uncertainties. The diagnosis of isomerism is typically made by echocardiography. However, multidetector computed tomography and MRI can help in obtaining detailed data on the morphology of the heart, great vessels, the anatomy of the internal organs, and their mutual arrangement that make an accurate diagnosis of heterotaxy syndrome.The authors present here the imaging findings of the heterotaxy polysplenia syndrome in a 21-year-old female with a complete endocardia cushion defect and a duplicated right renal vein.
Databáze: Directory of Open Access Journals