Excision of bilateral pheochromocytomas followed by staged resection of neuroendocrine carcinoma of the pancreas

Autor: Sandesh V. Parelkar, Rujuta S. Shah, Sanjay N. Oak, Beejal V. Sanghvi, Gayatri Munghate, Satej S. Mhaskar, D.V. Kulkarni, Rahul Kumar Gupta, Kedar P. Mudkhedkar, Deepa P. Makhija, K.K. Khidtta
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Journal of Pediatric Surgery Case Reports, Vol 58, Iss , Pp - (2020)
Druh dokumentu: article
ISSN: 2213-5766
DOI: 10.1016/j.epsc.2020.101463
Popis: Pheochromocytoma (PCC) and Pancreatic Neuroendocrine tumor (PNET) occurring together have been considered as a spectrum of Von Hippel Lindau (VHL) Syndrome and carries a grave prognosis. Considering the rarity of the disease, there is a wide range of presentations, investigations and management options described in literature. We describe one such case that was managed by staged excision of bilateral pheochromocytoma followed by pancreatic neuroendocrine tumor with a five years follow up and also discuss in detail our review of literature about this condition.
Databáze: Directory of Open Access Journals