Autor: |
Sandesh V. Parelkar, Rujuta S. Shah, Sanjay N. Oak, Beejal V. Sanghvi, Gayatri Munghate, Satej S. Mhaskar, D.V. Kulkarni, Rahul Kumar Gupta, Kedar P. Mudkhedkar, Deepa P. Makhija, K.K. Khidtta |
Jazyk: |
angličtina |
Rok vydání: |
2020 |
Předmět: |
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Zdroj: |
Journal of Pediatric Surgery Case Reports, Vol 58, Iss , Pp - (2020) |
Druh dokumentu: |
article |
ISSN: |
2213-5766 |
DOI: |
10.1016/j.epsc.2020.101463 |
Popis: |
Pheochromocytoma (PCC) and Pancreatic Neuroendocrine tumor (PNET) occurring together have been considered as a spectrum of Von Hippel Lindau (VHL) Syndrome and carries a grave prognosis. Considering the rarity of the disease, there is a wide range of presentations, investigations and management options described in literature. We describe one such case that was managed by staged excision of bilateral pheochromocytoma followed by pancreatic neuroendocrine tumor with a five years follow up and also discuss in detail our review of literature about this condition. |
Databáze: |
Directory of Open Access Journals |
Externí odkaz: |
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