A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia

Autor: Veena Dronamraju, Kaitlyn McSurdy, Ryan Graham, Parth Rali, Maruti Kumaran, Daniela Proca, Bilal Lashari, Yoshiya Toyoda, Rohit Gupta
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Pulmonary Circulation, Vol 13, Iss 2, Pp n/a-n/a (2023)
Druh dokumentu: article
ISSN: 2045-8940
DOI: 10.1002/pul2.12214
Popis: Abstract Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID‐19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately.
Databáze: Directory of Open Access Journals