Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association

Autor:	A.R. de Santana, M.D.L. Castro de Oliveira Figueirôa, A.L. Souza Pedreira, G.L. Behrens Pinto, M.B. Santiago
Jazyk:	English<br />Italian
Rok vydání:	2024
Předmět:	IgG4-related disease adult-onset xanthogranuloma orbit Medicine Internal medicine RC31-1245
Zdroj:	Reumatismo, Vol 76, Iss 1 (2024)
Druh dokumentu:	article
ISSN:	0048-7449 2240-2683
DOI:	10.4081/reumatismo.2024.1641
Popis:	Adult-onset xanthogranuloma (AOX) and immunoglobulin G4-related disease (IgG4-RD) are uncommon fibrosing conditions that may exhibit localized ocular manifestations and occasionally systemic symptoms. These conditions exhibit overlapping clinical and histological features, suggesting a potential correlation between them, although their exact relationship remains unclear. This paper presents the case of a black male patient exhibiting typical histological indications of both AOX and IgG4-RD. The patient responded positively to corticosteroid treatment.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/0b30c9cf919a41f69222af2e4a232091 Zobrazit plný text záznamu View record in DOAJ