| Autor: |
Carlos A. Hinojosa, Javier E. Anaya-Ayala, Hugo Laparra-Escareno, Rene Lizola, Adriana Torres-Machorro |
| Jazyk: |
English<br />Korean |
| Rok vydání: |
2017 |
| Předmět: |
|
| Zdroj: |
Vascular Specialist International, Vol 33, Iss 3, Pp 112-116 (2017) |
| Druh dokumentu: |
article |
| ISSN: |
2288-7970 |
| DOI: |
10.5758/vsi.2017.33.3.112 |
| Popis: |
Marfan syndrome is a connective tissue disorder associated with aortic dissection, aneurysmal degeneration and rupture. These cardiovascular complications represent the main cause of mortality, therefore repair is indicated. We present a 35-year-old woman who experienced acute onset of chest pain. Her imaging revealed a chronic DeBakey type I dissection with aortic root dilation and descending thoracic aneurysmal degeneration. She underwent a Bentall procedure and endovascular exclusion of the descending thoracic aortic aneurysm. She was closely followed and 2 years later a computed tomography angiography (CTA) revealed the aneurysmal degeneration of the thoracoabominal aorta and bilateral iliac arteries. The patient underwent a composite reconstruction using multi-visceral branched and bifurcated Dacron grafts. At 5 years from her last surgery, a CTA revealed no new dissection or further aneurysmal degenerations. Aortic disease in Marfan patients is a complex clinical problem that may lead to secondary or tertiary aortic reconstructions; close follow-up is mandatory. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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