Pseudo-Bartter Syndrome in Patients with Cystic Fibrosis and Clinical Features

Autor: Mehmet Mustafa Özaslan, Handan Duman Şenol, Meral Barlık, Fevziye Çoksüer, Bahar Dindar, Esen Demir, Figen Gülen
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Journal of Behçet Uz Children's Hospital, Vol 13, Iss 2, Pp 94-100 (2023)
Druh dokumentu: article
ISSN: 2822-4469
DOI: 10.4274/buchd.galenos.2023.44520
Popis: Objective: Pseudo-Bartter syndrome (PBS) is a complication of cystic fibrosis (CF) accompanied by electrolyte disorders. We aimed to compare the clinical features of patients diagnosed with CF with or without PBS in our clinic. Method: One hundred twenty-eight patients with the diagnosis CF data was recorded. Clinical features, diagnostic test results, colonization status, complications and genetic test results were compared in patients with and without PBS. Results: Totally 128 patients who were regularly followed diagnosis CF January 2017 and May 2022 and 18 of them (14%) developed PBS. Median age of CF diagnosis was significantly lower in patients with PBS (p
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