Steroid-responsive Encephalopathy Associated with Autoimmune Thyroiditis (SREAT) Presenting with Pure Cerebellar Ataxia

Autor: Pichet Termsarasab, Yuvadee Pitakpatapee, Steven J. Frucht, Prachaya Srivanitchapoom
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Tremor and Other Hyperkinetic Movements, Pp 1-7 (2018)
Druh dokumentu: article
ISSN: 2160-8288
DOI: 10.7916/D8CZ4QQQ
Popis: Background: Myoclonus and tremor are common movement disorder phenomenologies in steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT). Pure ataxia without encephalopathy has rarely been reported. Case report: We report 21- and 40-year-old females who presented with subacute pure ataxia without encephalopathy. After immunotherapies, both exhibited initial improvement of ataxia, and subsequently remained in plateau phase. Discussion: This treatable disorder should be added to the differential diagnoses of progressive cerebellar ataxia, and anti-thyroid peroxidase and anti-thyroglobulin should be considered as part of the workup. It is crucial not to misdiagnose SREAT presenting with pure cerebellar ataxia as degenerative or spinocerebellar ataxia.
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