Cardiogenic Shock: An Unusual Initial Presentation of Churg-Strauss Syndrome

Autor: M. Apirami, J. A. Pratheepan, T. Kumanan, M. Guruparan, G. Selvaratnam
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Case Reports in Rheumatology, Vol 2018 (2018)
Druh dokumentu: article
ISSN: 2090-6889
2090-6897
DOI: 10.1155/2018/2076837
Popis: Churg-Strauss syndrome (CSS) is a rare autoimmune condition, characterized by necrotizing extravascular eosinophil rich granulomatous inflammation of the tissues and disseminated small-medium sized vessel vasculitis in a patient with bronchial asthma and tissue eosinophilia. Though pulmonary involvement is the predominant feature of CSS, extra pulmonary involvement, in particular, cardiac involvement, denotes an adverse outcome. Here we report a 50-year-old female who presented with cardiogenic shock due to an acute coronary event as the initial manifestation of CSS. A subsequent coronary angiogram revealed normal epicardial coronaries. She was a patient with bronchial asthma and developed vasculitic rash, bilateral sensory motor polyneuropathy, and migratory peripheral lung field shadows in the background of peripheral eosinophilia during the course of the illness. She was diagnosed as having CSS based on ACR criteria and aggressively treated with immunosuppressants according to her Five-Factor Score and has shown prompt response to therapy. This case report adds to the literature another rare initial presentation of CSS to the existing array of its clinical manifestations.
Databáze: Directory of Open Access Journals
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