Serial lymphoscintigraphic findings in a patient with Gorham's disease with lymphedema
| Autor: | Baulieu F, De Pinieux G, Annabel Maruani, Vaillant L, Lorette G |
|---|---|
| Přispěvatelé: | Centre Hospitalier Régional Universitaire de Tours (CHRU Tours), Centre Hospitalier Régional Universitaire de Tours (CHRU de Tours), Université Francois Rabelais [Tours], Infectiologie et Santé Publique (UMR ISP), Institut National de la Recherche Agronomique (INRA)-Université de Tours (UT), CHU Trousseau [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Centre Hospitalier Régional Universitaire de Tours (CHRU TOURS), Institut National de la Recherche Agronomique (INRA)-Université de Tours |
| Rok vydání: | 2014 |
| Předmět: |
Male
Tomography Emission-Computed Single-Photon Time Factors Lymphangioma Biopsy SPECT/CT Prognosis Multimodal Imaging lymphangiomatosis body regions Lower Extremity Gorham's disease Predictive Value of Tests Disease Progression Humans LOWER-LIMB LYMPHEDEMA Osteolysis Essential Whole Body Imaging Lymphedema BONE Child Tomography X-Ray Computed [SDV.MHEP]Life Sciences [q-bio]/Human health and pathology Lymphoscintigraphy |
| Zdroj: | Lymphology Lymphology, Charles l Witte Md, 2014, 47 (3), pp.118-122 Europe PubMed Central |
| ISSN: | 0024-7766 |
| Popis: | International audience; Gorham's disease is a rare disorder characterized by vascular, "lymphangiomatous" and/or "hemangiomatous" lesions in bone and surrounding soft tissues. Associated lymphedema has not been reported and clinical evolution is unpredictable. Plain radiographs, CT, MRI, and occasionally bone scintigraphy, are used to detect the bone and soft tissues changes. Biopsy is a major component of the diagnostic process. We report the findings of serial lymphoscintigraphy in a young boy with a polyostotic Gorham's disease associated with lymphangioma of the thigh and lower limb lymphedema. In this patient, lymphoscintigraphy was useful for diagnosis and follow-up of primary lymphedema. It provided valuable information concerning the occurrence, location, and progression of lymphatic lesions in both bone and soft tissues. |
| Databáze: | OpenAIRE |
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