Peutz-Jeghers Syndrome Complicated with Intussusception: Enteroscopic Polyps Resections through Laparotomy

Autor: Zdravko, Perko, Dragan, Krnić, Zenon, Pogorelić, Nikica, Druzijanić, Miroslav, Simunić, Kanito, Bilan, Damir, Kraljević, Marina Maras, Simunić
Jazyk: angličtina
Rok vydání: 2013
Předmět:
Zdroj: Collegium antropologicum
Volume 37
Issue 1
ISSN: 1848-9486
0350-6134
Popis: Peutz-Jeghers syndrome is an autosomal dominant inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous pigmentations. Here we present a case of a 30-year-old woman who was hospitalized and underwent diagnostic procedures because of crampy adbdominal pain. Physical examination on admission revealed pigmented spots around lips and on the oral mucosa. Multiple polyps were found in stomach, small and large intestine, with signs of initial ileo-ileal intussusception. After endoscopic removal of achievable polyps, we applied gastroscope through laparotomy and enterotomy and removed total number of 34 polyps from small bowell. The polyps were found to be mostly hamartomatous at histological examination. This procedure can provide removal of the most polyps, which are potentially premalignant, also with less complicationes than after multiple intestinal resectiones.
Databáze: OpenAIRE