[Congenital haemorrhagic diseases]
| Autor: | Jean-Francois Schved |
|---|---|
| Přispěvatelé: | Nowak, Cécile, Département d'hématologie biologique[Montpellier], Université Montpellier 1 (UM1)-Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier)-CHU Saint-Eloi, Université de Montpellier (UM) |
| Jazyk: | francouzština |
| Rok vydání: | 2015 |
| Předmět: |
[SDV.MHEP.HEM] Life Sciences [q-bio]/Human health and pathology/Hematology
congenital hereditary and neonatal diseases and abnormalities Hemostasis Blood Coagulation Disorders Inherited hemic and lymphatic diseases Humans [SDV.MHEP.HEM]Life Sciences [q-bio]/Human health and pathology/Hematology Hemorrhagic Disorders Blood Coagulation Factors |
| Zdroj: | Europe PubMed Central Revue du Praticien (La) Revue du Praticien (La), J B Bailliere et Fils, 2015, 65 (5), pp.613-7 |
| ISSN: | 0035-2640 |
| Popis: | International audience; Congenital haemorrhagic diseases are the consequences of haemostasis dysfunction or defects. Among primary haemostasis disorders, von Willebrand disease is the most frequent. Hopefully the type 1 von Willebrand disease, which affects 85% of patients, is generally a mild haemorrhagic disorder. However it may induce some troubles during the everyday life. On the other side, haemophilia is the most frequent congenital coagulation disorders. Haemophilia A is due a factor VIII deficiency while haemophilia B is due to a factor IX deficiency. Haemophilia is mainly a musculoskeletal disease. Recurrent joint bleedings may lead to a severe disabling arthropathy. The organization of care for hemophilia is managed by haemophilia treatment centers. Other rare bleeding disorders may lead to the same complications but requires specific treatments. |
| Databáze: | OpenAIRE |
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