Surgical aspects of intussusception secondary to Peutz-Jeghers syndrome
| Autor: | Carlos Baeza-Herrera, Luis Manuel García-Cabello, Heladio M. Nájera-Garduño, Luis Ángel Sánchez-Fernández, Francisco Mora-Hernández, Alejandra I. Ortiz-Zúñiga |
|---|---|
| Rok vydání: | 2005 |
| Předmět: |
intussusception
Male Radiography Abdominal congenital hereditary and neonatal diseases and abnormalities Peutz-Jeghers syndrome Laparotomy Ileocecal Valve Adolescent Medicina Ileal Diseases Ileostomy Peutz-Jeghers Syndrome Jejunal Diseases intestinal polyposis acute abdomen Treatment Outcome children Child Preschool Jeghers syndrome Peutz Humans Female skin and connective tissue diseases Child Intussusception |
| Zdroj: | Universidad Nacional Autónoma de México UNAM Redalyc-UNAM Cirugía y Cirujanos (México) Num.2 Vol.73 |
| ISSN: | 0009-7411 |
| Popis: | Peutz-Jeghers syndrome (PJS) is a familial condition characterized by the presence of pigmented mucocutaneous spots and intestinal polyposis. Intussusception is the most frequent abdominal complication, but it is very rare. In our country, this is the second known report. In this article we present four cases of PJS associated with intussusception. All the patients were female and all underwent a surgical procedure. The intussusception was located in the ileum and colon. There are no more than 20 reported cases in the world where these two entities are associated. Children with PJS have a high risk of suffering from ileo-ileal or jejuno-ileal intussusception that will frequently require a special surgical procedure. |
| Databáze: | OpenAIRE |
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