| Autor: |
Analía, Elguezabal Rodriguez, Miriam, Gené Hijós, Aleidis, Caro Tarragó, Salomé, Martínez González |
| Rok vydání: |
2010 |
| Předmět: |
|
| Zdroj: |
Gastroenterologia y hepatologia. 34(6) |
| ISSN: |
0210-5705 |
| Popis: |
Fibromatosis consists of a benign fibroblastic proliferation with local infiltrative growth. Two types are recognized: a superficial and a deep form, also known as desmoid tumor. The latter may occur sporadically or in association with familial adenomatous polyposis and Gardner's syndrome. Pancreatic presentation is exceptional and only eight cases have been described in the literature.We report the case of a 29-year-old woman with a history of familial colonic polyposis and two pancreatic lesions. In the surgical specimen, two poorly defined pancreatic lesions were observed with infiltration of neighboring organs. Histologically, the lesions corresponded to mesenchymal proliferation with a fusocellular pattern without cytological atypica, which were diagnosed as desmoid tumors.The etiology of fibromatosis is unknown. In patients with familial colonic polyposis, the most common localization of desmoid tumor is intra-abdominal. Pancreatic presentation is unusual, requiring differential diagnosis with other pancreatic neoplasms. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
|
