Value of Doppler sonography in the assessment of patients with Caroli's disease

Autor:	W, Gorka, D B, Lewall
Rok vydání:	1998
Předmět:	Adult Liver Cirrhosis Male Time Factors Portal Vein Hemodynamics Infant Caroli Disease Child Preschool Hypertension Portal Humans Female Prospective Studies Ultrasonography Doppler Color Child
Zdroj:	Journal of clinical ultrasound : JCU. 26(6)
ISSN:	0091-2751
Popis:	We examined the intracystic flow pattern and portal hemodynamics with Doppler sonography in patients with Caroli's disease.Sonographic characteristics and portal hemodynamics were studied by color Doppler sonography and spectral analysis in 5 patients (4 children and 1 adult) with Caroli's disease using high-frequency transducers. Caroli's disease was associated with infantile polycystic kidney disease in 4 patients and congenital hepatic fibrosis in 2 patients. Four patients had no clinical or imaging evidence of portal hypertension. The adult patient had congenital hepatic fibrosis and portal hypertension.Color Doppler sonograms and spectral analyses disclosed distinctive hepatic arterial and portal venous flow within the fibrovascular projections in the bile ducts of all the children. The adult with advanced portal hypertension presented with a no-flow state in the intracavitary part of the portal vein and a strong arterial signal related to disturbed hemodynamics in the arterialized liver.The fact that portal hemodynamics change over time should be taken into account when Doppler assessment of Caroli's disease is attempted. Doppler sonographic monitoring of the portal system to indirectly diagnose and follow the progression of so-called congenital hepatic fibrosis may be an effective alternative to liver biopsy.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=pmid________::b77d1347a480aa74bed06606b1bd6fae https://pubmed.ncbi.nlm.nih.gov/9641387 Zobrazit plný text záznamu Plný text