| Autor: |
Khurram, Akhtar, Mehboob, Sultan, Waqar, Ahmed, Maad, Ullah, Nadeem, Sadiq |
| Rok vydání: |
2012 |
| Předmět: |
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| Zdroj: |
Journal of the College of Physicians and Surgeons--Pakistan : JCPSP. 24 |
| ISSN: |
1681-7168 |
| Popis: |
Pentalogy of Cantrell with ectopia cordis is a rare congenital anomaly, first described in 1958 by Cantrell, has a reported incidence of around 5-10 cases per one million live births with wide variety of clinical presentations. We are reporting a child with ectopia cordis along with cleft lower sternum, upper abdominal wall defect, ectopic umbilicus and diaphragmatic defect. Echocardiography in first month of life revealed a restrictive perimembranous ventricular septal defect and a small patent Foramen Ovale, both closed spontaneously in infancy. CT angiography at 10 months of age revealed a defect in the thoracic and abdominal walls along with herniation of left ventricular apex into epigastrium. The two ventriculi formed a tail that looked like a crocodile. This patient underwent surgical correction at our institution at 14 months of age and recovered well with no residual issue. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
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