Pulmonary capillary haemangiomatosis: a rare cause of pulmonary hypertension

Autor: K Anand, Babu, K, Supraja, Raj B, Singh
Rok vydání: 2015
Předmět:
Zdroj: The Indian journal of chest diseasesallied sciences. 56(4)
ISSN: 0377-9343
Popis: Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy.
Databáze: OpenAIRE