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Background: Optic pathway gliomas are rare, but the most common primary tumours of the optic nerve. They affect children more than adults. Management of these patients requires an individualized and multidisciplinary approach. Case report: A clinical course and ophthalmological, electrophysiological, neuroradiological, neurosurgical and paediatric-oncological management of an extensive optic pathway glioma in a teenager with unspecific visual problems are presented. Conclusions: Although most frequently low grade astrocytomas, optic pathway gliomas follow a highly variable and unpredictable clinical course. Therefore, their optimal management is still controversial. In the last decade, chemotherapy has become the first-line treatment modality, especially in inoperable and/or extended gliomas. Izhodišča: Gliomi vidne poti so redki, vendar najpogostejši primarni tumorji vidnega živca, ki prizadenejo otroke pogosteje kot odrasle. Njihova obravnava zahteva individualizirani in multidisciplinarni pristop. Prikaz primera: V prispevku je predstavljen klinični potek in oftalmološka, elektrofiziološka, nevroradiološka, nevrokirurška ter onkološko pediatrična obravnava razširjenega glioma vidne poti pri najstniku z nespecifičnimi motnjami vida. Zaključki: Čeprav so gliomi vidne poti najpogosteje nizko maligni astrocotomi, je njihov klinični potek zelo različen in nepredvidljiv, zaradi česar njihovo optimalno zdravljenje še vedno ni povsem dorečeno. V zadnjem desetletju je postalo zdravljenje prve izbire kemoterapija, še posebej pri neoperabilnih in/ali razširjenih gliomih. |
