| Autor: |
Ebels, T, Dapper, F, Bohle, RM, Hagel, KJ, Nikkels, PGJ, Hehrlein, FW |
| Přispěvatelé: |
Cardiovascular Centre (CVC) |
| Jazyk: |
angličtina |
| Rok vydání: |
1997 |
| Předmět: |
|
| Zdroj: |
Cardiology in the young, 7(4), 402-409. Cambridge University Press |
| ISSN: |
1047-9511 |
| Popis: |
Aortic atresia is rare in the setting of a normally developed left ventricle with a ventricular septal defect. In this combination, as far as we know, it has been described only with concordant ventriculo-arterial connections, for which seven one-stage biventricular repairs have now been described. We describe here the case of a 3 1/2-month-old male infant with a similar combination but with discordant ventriculo-arterial connections and severe pulmonary hypertension. It was the right ventricle which achieved normal size in this arrangement, presumably because of the ventricular septal defect. One-stage biventricular correction was accomplished, employing a single pulmonary allograft, aided by massive doses of Prostaglandin E1. As far as we know this is the first report of the combination of aortic atresia, discordant ventriculo-arterial connections, a ventricular septal defect and balanced ventricles. We complement our surgical account, nonetheless, with a description of a comparable specimen from our anatomic museum. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
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