IgG4関連硬化性疾患と考えられた後腹膜線維症の1例

Autor: Minato, Noriko, Takayama, Hitoshi, Mukai, Masatoshi, Miyagawa, Yasushi, Tsujihata, Masao, Nonomura, Norio, Okuyama, Akihiko
Jazyk: japonština
Rok vydání: 2010
Předmět:
Zdroj: 泌尿器科紀要. 56(7):371-375
ISSN: 0018-1994
Popis: A 67-year-old man had undergone a right ureteronephrectomy because of a right ureter tumor, but the pathological diagnosis was inflammatory tissue with plasma cells, lymphocytes, and fibrosis. About 3 years later, abdominal computed tomography (CT) revealed a solid tumor at the left renal hilus. We resected the tumor and the pathological diagnosis was the same as before. More than 2 years later, because of elevated pancreatic enzymes, immunoglobulin G (IgG) and IgG4, more detailed examinations ware done, and he was diagnosed with IgG4-related autoimmune pancreatitis. We believe that the retroperitoneal tumor was retroperitoneal fibrosis associated with IgG4-related sclerosing disease. Now, he is being treated with steroid therapy. IgG4-related sclerosing disease is a systemic disease whose concept is now being established. Much more work is needed to understand this disease.
Databáze: OpenAIRE