Therapeutic management of ventricular arrhythmias in Andersen-Tawil syndrome
| Autor: | Lara Baduena, Giulia Careri, Emanuela Facchini, Umberto Parravicini, Valeria Sansone, Luca Bergamasco, Paola Paffoni, Stefano Maffè, Nicolò Franchetti Pardo, Franco Zenone, Pierfranco Dellavesa |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
medicine.medical_specialty
medicine.medical_treatment 030204 cardiovascular system & hematology Asymptomatic Sudden death 03 medical and health sciences Electrocardiography 0302 clinical medicine Pharmacotherapy Andersen–Tawil syndrome Internal medicine medicine Humans cardiovascular diseases 030212 general & internal medicine Flecainide Andersen Syndrome business.industry Periodic paralysis medicine.disease Implantable cardioverter-defibrillator Defibrillators Implantable Death Sudden Cardiac Ventricular fibrillation cardiovascular system Cardiology Tachycardia Ventricular medicine.symptom Cardiology and Cardiovascular Medicine business Anti-Arrhythmia Agents medicine.drug |
| Zdroj: | Journal of electrocardiology. 58 |
| ISSN: | 1532-8430 |
| Popis: | Andersen-Tawil Syndrome (ATS) is a rare periodic paralysis with typical skeletal and neuromuscular features. Cardiac involvement may range from asymptomatic ventricular arrhythmias to sudden death. Its management remains challenging and the choice between antiarrhythmic drug therapy and implantable cardioverter defibrillator (ICD) is not simple. We present a case of ATS patient with episodes of bidirectional ventricular tachycardia, well controlled by flecainide therapy initially, which in particular conditions of fever and hypokaliemia had a cardiac arrest with ventricular fibrillation, with neurological sequelae and need of an ICD implant. A review of the therapeutic management of this disease is presented. |
| Databáze: | OpenAIRE |
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