Megacystis?microcolon?intestinal hypoperistalsis and prune belly: overlapping syndromes
| Autor: | Netta M. Blitman, Terry L. Levin, Carlos Vega-Rich, Lamia Soghier, Suhas Nafday |
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| Rok vydání: | 2004 |
| Předmět: |
Male
Radiography Abdominal Intestinal pseudo-obstruction medicine.medical_specialty Colon Urinary Bladder Gastroenterology Diagnosis Differential Abdominal wall Prune belly syndrome Internal medicine Prune belly medicine Humans Prune Belly Syndrome Radiology Nuclear Medicine and imaging Hydronephrosis Ultrasonography business.industry Intestinal Pseudo-Obstruction Infant Newborn Anatomy Megacystis Microcolon medicine.disease Intestines medicine.anatomical_structure Pediatrics Perinatology and Child Health Peristalsis business Hypoperistalsis |
| Zdroj: | Pediatric Radiology. 34:995-998 |
| ISSN: | 1432-1998 0301-0449 |
| DOI: | 10.1007/s00247-004-1260-2 |
| Popis: | Megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) is a rare, often fatal condition. Infants present with a functional obstruction of the gastrointestinal tract (GI), malrotation, microcolon, and a large nonobstructed bladder. Several features common to both MMIHS and Eagle-Barrett or prune belly syndrome (PBS) include hydronephrosis, bladder distension and laxity of the abdominal wall musculature. Additionally, MMIHS and PBS have been reported in the same family, suggesting the possibility of a common pathogenesis. MMIHS usually presents in female infants. We present a male infant diagnosed with both MMIHS and PBS. This is a unique case in which both MMIHS and true PBS are present in the same infant. |
| Databáze: | OpenAIRE |
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