Limb lengthening and correction of deformity in the lower limbs of children with osteogenesis imperfecta
| Autor: | James A. Fernandes, Michael J. Bell, K.A.N. Saldanha, M. Saleh |
|---|---|
| Rok vydání: | 2004 |
| Předmět: |
Male
medicine.medical_specialty Adolescent medicine.medical_treatment Osteogenesis Distraction Ilizarov Technique Bone Nails law.invention Intramedullary rod law medicine Deformity Humans Orthopedics and Sports Medicine Femur Tibia Child Wound Healing business.industry Equipment Design Osteogenesis Imperfecta medicine.disease Osteochondrodysplasia Leg Length Inequality Surgery Treatment Outcome Osteogenesis imperfecta Orthopedic surgery Distraction osteogenesis Female medicine.symptom business |
| Zdroj: | The Journal of Bone and Joint Surgery. British volume. :259-265 |
| ISSN: | 2044-5377 0301-620X |
| DOI: | 10.1302/0301-620x.86b2.14393 |
| Popis: | We performed limb lengthening and correction of deformity of nine long bones of the lower limb in six children (mean age, 14.7 years) with osteogenesis imperfecta (OI). All had femoral lengthening and three also had ipsilateral tibial lengthening. Angular deformities were corrected simultaneously. Five limb segments were treated using a monolateral external fixator and four with the Ilizarov frame. In three children, lengthening was done over previously inserted femoral intramedullary rods. The mean lengthening achieved was 6.26 cm (mean healing index, 33.25 days/cm). Significant complications included one deep infection, one fracture of the femur and one anterior angulation deformity of the tibia. The abnormal bone of OI tolerated the external fixators throughout the period of lengthening without any episodes of migration of wires or pins through the soft bone. The regenerate bone formed within the time which is normally expected in limb-lengthening procedures performed for other conditions. We conclude that despite the abnormal bone characteristics, distraction osteogenesis to correct limb-length discrepancy and angular deformity can be performed safely in children with OI. |
| Databáze: | OpenAIRE |
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