Noncompaction cardiomyopathy: Manifestation as a surgical pitfall – rare but real
| Autor: | Pradeep Vaideeswar, Arivarsan Karunamurthy, Roneil Parikh, Balaji Aironi, Prashant Mishra, Nandkishor Agrawal, Supreet P Marathe |
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| Rok vydání: | 2014 |
| Předmět: |
Male
Pulmonary and Respiratory Medicine Noncompaction cardiomyopathy medicine.medical_specialty Treatment outcome Cardiomyopathy Autopsy Postoperative Complications Predictive Value of Tests Risk Factors Internal medicine Humans Medicine Cardiac Surgical Procedures Child Ultrasonography Isolated Noncompaction of the Ventricular Myocardium business.industry Myocardium Infant General Medicine Middle Aged medicine.disease Treatment Outcome Child Preschool Predictive value of tests Heart failure Cardiology Female Surgery Cardiology and Cardiovascular Medicine business |
| Zdroj: | Asian Cardiovascular and Thoracic Annals. 23:133-139 |
| ISSN: | 1816-5370 0218-4923 |
| DOI: | 10.1177/0218492314533559 |
| Popis: | Objectives Noncompaction cardiomyopathy is characterized by hyper-trabeculation of the myocardium. The patients present with heart failure and variable combination of arrhythmias and thromboembolism. Although several articles have shed light on the medical aspect of this disease, none have highlighted its surgical relevance. A death following ligation of a patent ductus arteriosus prompted us to evaluate the surgical aspects of this disease. Methods Autopsy records from 2003 to 2012 were reviewed, and cases identified as noncompaction cardiomyopathy were retrieved and analyzed. Cases with obligatory hyper-trabeculation were excluded. Results Thirteen patients were found to have noncompaction cardiomyopathy in 9427 autopsies performed. Their ages ranged from 4 months to 55 years; 10 were children, and all 3 adults were over 45 years of age. Only one patient had an antemortem diagnosis of noncompaction cardiomyopathy on echocardiography. There were 7 postoperative deaths. Conclusions Although noncompaction cardiomyopathy is rare, missing its diagnosis in a patient operated on for another indication can spell disaster postoperatively. As the clinical picture is nonspecific and the disease is not very well known, it needs vigilance on the part of the echocardiographer and surgeon. |
| Databáze: | OpenAIRE |
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