A fourth ventricular ganglioneurocytoma representing with cerebellar epilepsy: A case report and review of the literature
| Autor: | Adnan Dagcinar, Ahmet Hilmi Kaya, Zafer Sabancilar, Aydin Sav, Haydar Ali Taşdemir, Enis Kuruoglu |
|---|---|
| Rok vydání: | 2007 |
| Předmět: |
Cerebellum
medicine.medical_specialty Fourth ventricle Lesion Epilepsy medicine Humans Cerebellar Neoplasms Motor skill Fourth Ventricle medicine.diagnostic_test Infant Ganglioneuroma Magnetic resonance imaging General Medicine medicine.disease Magnetic Resonance Imaging Surgery medicine.anatomical_structure Anesthesia Pediatrics Perinatology and Child Health Female Neurology (clinical) Eyelid medicine.symptom Tomography X-Ray Computed Psychology Hemifacial spasm |
| Zdroj: | European Journal of Paediatric Neurology. 11:257-260 |
| ISSN: | 1090-3798 |
| DOI: | 10.1016/j.ejpn.2007.02.005 |
| Popis: | Fourth ventricular low-grade tumoral or dysplastic neuronal lesions have been reported as an epileptic focus for recently described cerebellar epilepsy in the form of repetitive and stereotyped attacks of hemifascial spasm, eye blinking, fascial movements, head deviation and dysautonomic manifestations. The case of a 3-month old infant having fourth ventricular mass with similar symptoms such as paroxysmal facial movements, eye blinking, eyelid contractions and abnormal head posture is reported in this article. After a few days of her admission, her attacks displayed a new form with altered consciousness and left limb jerks which were unresponsive to medical therapy. Following the surgical excision of the lesion 10 months ago, attacks disappeared and she is still seizure free. Histopathological diagnosis was ganglioneurocytoma. The seizures (which may be intractable in cerebellar epilepsy) are thought to have arisen from subcortical structures such as cerebellum, brain stem nuclei or the lesion itself. In the case of intractable episodes, surgical excision may prevent further seizures and help patients have a normal cognitive and motor development. |
| Databáze: | OpenAIRE |
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