Pulmonary Ewing Sarcoma/Primitive Neuroectodermal Tumor: A Case Report and a Review of the Literature
| Autor: | Juan Suárez Antelo, Carlota Rodríguez García, Carmen Montero Martínez, Héctor Verea Hernando |
|---|---|
| Rok vydání: | 2010 |
| Předmět: |
Leiomyosarcoma
Pathology medicine.medical_specialty Lung Neoplasms business.industry Sarcoma Ewing General Medicine medicine.disease Synovial sarcoma Young Adult Primitive neuroectodermal tumor Humans Neuroectodermal Tumors Primitive Medicine Outpatient clinic Female Angiosarcoma Sarcoma business Rhabdomyosarcoma Etoposide medicine.drug |
| Zdroj: | Archivos de Bronconeumología ((English Edition)). 46:44-46 |
| ISSN: | 1579-2129 |
| DOI: | 10.1016/s1579-2129(10)70009-4 |
| Popis: | Primary thoracic sarcomas are very rare. The most common intrathoracic variants are synovial sarcoma, angiosarcoma, leiomyosarcoma, rhabdomyosarcoma, and sarcomatoid mesothelioma. Although thoracic Ewing sarcoma/primitive neuroectodermal tumor (PNET) usually develops on the chest wall, there have been reports of primary Ewing sarcoma/PNET of the lung. We present the case of a 22-year-old woman with Ewing sarcoma/PNET diagnosed following histologic, immunohistochemical, and in situ hybridization studies of a bronchial biopsy specimen. Radiography, ventilation-perfusion scintigraphy, and a bone marrow biopsy confirmed that the tumor was not metastatic. The patient was started on a chemotherapy regimen of vincristine, actinomycin, cyclophosphamide, doxorubicin, ifosfamide, and etoposide and responded well. She is now being seen regularly at our outpatient clinic. |
| Databáze: | OpenAIRE |
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