Oral neurofibrosarcoma associated with neurofibromatosis type I
| Autor: | Paul D. Garen, Brad W. Neville, John R. Hann, Ramesh Narang |
|---|---|
| Rok vydání: | 1991 |
| Předmět: |
Adult
medicine.medical_specialty Pathology Neurofibromatosis 1 Mandibular Neoplasms Malignancy Pathology and Forensic Medicine Neurofibrosarcoma medicine Humans Neurofibroma Neurofibromatosis General Dentistry Aged Maxillary Neoplasms Neurofibromatosis type I business.industry Cancer Prognosis medicine.disease Dermatology Treatment Outcome Female business |
| Zdroj: | Oral Surgery, Oral Medicine, Oral Pathology. 72:456-461 |
| ISSN: | 0030-4220 |
| DOI: | 10.1016/0030-4220(91)90560-y |
| Popis: | One of the most feared complications of neurofibromatosis type I (NF-I) is development of cancer, which is estimated to occur in about 5% of cases. The most common associated malignancy is the neurofibrosarcoma (NFS). HOwever, oral NFS in association with NF-I has rarely been reported. We report two cases of oral NFS arising in patients with NF-I. Both patients died of their tumors. Oral NFS arising in association with NF-I appears to have an extremely poor prognosis, as do these tumors at other sites of the body. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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