Complex Case of Aggressive Intra-abdominal Desmoid-type Fibromatosis Status Post Cholecystectomy
Autor: | Kshama Vyas, Manohar Roda, Juliana Sitta, Jigarkumar Rangunwala, Varsha Prakash |
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Rok vydání: | 2020 |
Předmět: |
aggressive desmoid tumor
medicine.medical_specialty desmoid tumor medicine.medical_treatment Scars 030204 cardiovascular system & hematology Familial adenomatous polyposis Metastasis 03 medical and health sciences 0302 clinical medicine unresectable desmoid tumor Gardner Syndrome Pathology medicine desmoid tumor status post cholecystectomy locally advanced desmoid tumor intra-abdominal fibromatosis medicine.diagnostic_test business.industry Fibromatosis General Engineering desmoid-type fibromatosis Gastric outlet obstruction Magnetic resonance imaging medicine.disease body regions General Surgery Cholecystectomy Radiology medicine.symptom business 030217 neurology & neurosurgery |
Zdroj: | Cureus |
ISSN: | 2168-8184 |
Popis: | Desmoid-type fibromatosis (DF), also known as desmoid tumor, is an extremely rare, benign, mesenchymal fibrous tumor with no potential for metastasis. It can arise from any part of the body, most commonly extra-abdominally. Intra-abdominal DF can present sporadically, in sites of previous trauma, surgical scars and irradiation, or in association with familial adenomatous polyposis and Gardner syndrome. Intra-abdominal DF is uncommon and especially rare after a common surgery like cholecystectomy. We report a rare case of a 67-year-old male who presented with a locally aggressive intra-abdominal DF in the gallbladder fossa, status post cholecystectomy. This progressively enlarging infiltrative enhancing solid mass in the gallbladder fossa on serial computed tomography and magnetic resonance imaging demonstrated gastric outlet obstruction, biliary obstruction, portal vein narrowing and encasement of hepatic artery. Diagnosis of DF in this postoperative setting was delayed and challenging due to uncharacteristic clinical presentation. Radiologists should be aware of this unusual diagnosis and spectrum of imaging findings to help in timely surgical management and planning. |
Databáze: | OpenAIRE |
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