Cystic Fibrosis Pulmonary Guidelines
Autor: | Randall L. Rosenblatt, Daniel Rosenbluth, Marcia Katz, Henry L. Dorkin, Patrick A. Flume, Moira L. Aitken, Michelle S. Howenstine, Manu Jain, David C. McGiffin, Joseph M. Pilewski, Ahmet Uluer, Craig W. Lillehei, Beryl J. Rosenstein, Hector H. Gutierrez, Terry B. White, James D. Acton, Randall K. Young, Thomas M. Egan, Kathryn A. Sabadosa, Steven Strausbaugh, Mary K Lester, Sally E. Mitchell, Douglas S. Holsclaw, Bruce C. Marshall, Mike Mulligan, David M. Orenstein, Donna Beth Willey-Courand, Peter J. Mogayzel, Susanna A. McColley, Souheil Saddekni, Melissa Chin, Lynne M. Quittell, Paul Mohabir, Christopher M. Oermann, James R. Yankaskas, Michael P. Boyle, Robert J. Kuhn, R. Duane Davis, Jill Fleige, Michael J. Rock, Elizabeth Tullis, Anne M Downs, James L. Cunningham, Peter J Murphy, John L. Colombo, Linda L. Wolfenden, Thomas W. Ferkol, Patricia M. Joseph, Jeffrey S. Wagener, George Z. Retsch-Bogart, Christopher H. Goss, Karen A. Robinson, Carlos Milla, Felix Ratjen, Michael S. Schechter, Patricia E. Burrows, Aruna Sannuti, Charles B. Huddleston, Robert L. Vender, Leslie Hazle, Mark J. Sands, Charles T. Burke, Wickii T. Vigneswaran, Ronald C. Rubenstein, Guillermo A. doPico, Jerry A. Nick, Wyn Hoover, Mark H. Wholey |
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Rok vydání: | 2010 |
Předmět: |
Pulmonary and Respiratory Medicine
Spirometry Hemoptysis medicine.medical_specialty Aircraft Cystic Fibrosis Delphi Technique Weight Lifting medicine.medical_treatment Decision Making Bronchial Arteries Critical Care and Intensive Care Medicine Severity of Illness Index Cystic fibrosis Positive-Pressure Respiration Bronchoscopy Intensive care Administration Inhalation Pulmonary fibrosis Secondary Prevention medicine Humans Lung transplantation Intensive care medicine Lung Pleurodesis Saline Solution Hypertonic Travel medicine.diagnostic_test business.industry Patient Selection Anti-Inflammatory Agents Non-Steroidal Respiratory disease Pneumothorax medicine.disease Embolization Therapeutic Anti-Bacterial Agents Hospitalization Chest Tubes business Lung Transplantation |
Zdroj: | American Journal of Respiratory and Critical Care Medicine. 182:298-306 |
ISSN: | 1535-4970 1073-449X |
Popis: | Cystic fibrosis (CF) is a recessive genetic disease characterized by dehydration of the airway surface liquid and impaired mucociliary clearance. As a result, individuals with the disease have difficulty clearing pathogens from the lung and experience chronic pulmonary infections and inflammation. There may be intermittent pulmonary exacerbations or acute worsening of infection and obstruction, which require more intensive therapies. Hemoptysis and pneumothorax are complications commonly reported in patients with cystic fibrosis.This document presents the CF Foundation's Pulmonary Therapies Committee recommendations for the treatment of hemoptysis and pneumothorax.The committee recognized that insufficient data exist to develop evidence-based recommendations and so used the Delphi technique to formalize an expert panel's consensus process and develop explicit care recommendations.The expert panel completed the survey twice, allowing refinement of recommendations. Numeric responses to the questions were summarized and applied to a priori definitions to determine levels of consensus. Recommendations were then developed to practical treatment questions based upon the median scores and the degree of consensus.These recommendations for the management of the patient with CF with hemoptysis and pneumothorax are designed for general use in most individuals but should be adapted to meet specific needs as determined by the individuals, their families, and their health care providers. It is hoped that the guidelines provided in this manuscript will facilitate the appropriate application of these treatments to improve and extend the lives of all individuals with cystic fibrosis. |
Databáze: | OpenAIRE |
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