Hepatocellular carcinoma in an adult patient with congenital absence of the portal vein type II: A case report
Autor: | Naoki Hama, Hiroki Bessho, Akio Ishihara, Motohiro Hirao, Atsushi Miyamoto, Kiyoshi Mori, Reishi Toshiyama, Eiji Mita, Shinya Kato, Hisashi Ishida, Masayuki Mano, Satoshi Tanaka |
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Jazyk: | angličtina |
Rok vydání: | 2020 |
Předmět: |
medicine.medical_specialty
Radiofrequency ablation Portal vein Case Report Case Reports RC799-869 law.invention 03 medical and health sciences 0302 clinical medicine law Medicine Superior mesenteric vein congenital absence of the portal vein Pathological congenital abnormalities Hepatology business.industry Gastroenterology Venous blood hepatocellular carcinoma Diseases of the digestive system. Gastroenterology medicine.disease Shunt (medical) Splenic vein 030220 oncology & carcinogenesis Hepatocellular carcinoma 030211 gastroenterology & hepatology Radiology business |
Zdroj: | JGH Open, Vol 4, Iss 4, Pp 766-768 (2020) JGH Open: An Open Access Journal of Gastroenterology and Hepatology |
ISSN: | 2397-9070 |
Popis: | Congenital absence of the portal vein (CAPV) is a rare malformation in which intestinal and splenic venous blood bypasses the liver and drains into systemic veins. CAPV is classified into two types based on the absence (type I) or presence (type II) of portal venous flow into the hepatic parenchyma and is associated with multiple other anomalies such as usually benign hepatic tumors. There have been only two case reports describing hepatocellular carcinoma (HCC) in patients with CAPV type II to date. We report the third such patient. A 50‐year‐old woman was referred to our hospital for management of a giant hepatic tumor. Contrast‐enhanced computed tomography (CECT) indicated a huge mass occupying the right lobe of the liver; the radiological diagnosis was HCC. CECT also demonstrated that the superior mesenteric vein (SMV) and the splenic vein (SpV) joined to form a shunt draining into the left renal vein and that a hypoplastic portal vein branched from the confluence of the SMV and SpV and drained into the liver, indicating that the CAPV was type II. Liver resection was successfully performed to treat the HCC, and the pathological diagnosis was well‐differentiated HCC. Seven months after the operation, a recurrent small HCC was detected and treated with radiofrequency ablation without complications. The patient has been carefully followed for 6 months to date without any evidence of further recurrence. Patients with CAPV are predisposed to developing HCC and require close surveillance. A 50‐year‐old woman was diagnosed with a giant hepatocellular carcinoma (HCC) that was associated with congenital absence of the portal vein (CAPV) type II. Patients with CAPV type II are predisposed to developing HCC and require close surveillance. |
Databáze: | OpenAIRE |
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