| Popis: |
Cornelia de Lange Syndrome (CdLS) is a rare genetic disease characterized by several congenital anomalies including craniofacial, cardiovascular, genitourinary and musculoskeletal system. In CdLS, motor and mental retardation, short neck, microcephaly, micrognathia, high palate, hypertrichosis, typical facial appearance, various extremity abnormalities, gastrointestinal and cardiac anomalies may be present. The management of anesthesia in these patients can become very complex as it affects many systems. We aimed to discuss the cases that should be considered during anesthesia in pediatric cleft palate surgery with CdLS, as there are few case reports in the literature on the anesthetic management of these patients. |
