Successful preterm pregnancy in a rare variation of Herlyn-Werner-Wunderlich syndrome: a case report

Autor: Emilio Piccione, Maria Giovanna Salerno, Francesco Cucinelli, Luisa Casadei, Stefania Cappello, Eleonora Piccolo
Rok vydání: 2018
Předmět:
Fetal Membranes
Premature Rupture
Ectrodactyly
medicine.medical_treatment
Utero didelphys
Obstructed hemivagina
Case Report
Müllerian duct anomalies
Herlyn-Werner-Wunderlich syndrome (HWWS)
OHVIRA syndrome
Pregnancy
Renal agenesis
Kidney
0302 clinical medicine
Gynecologic Surgical Procedures
Salpingectomy
030219 obstetrics & reproductive medicine
Obstetrics
Obstetrics and Gynecology
Gestational age
Treatment Outcome
030220 oncology & carcinogenesis
Vagina
Female
Kidney Diseases
Presentation (obstetrics)
Adult
medicine.medical_specialty
Abdominal Abscess
Limb Deformities
Congenital
lcsh:Gynecology and obstetrics
Congenital Abnormalities
03 medical and health sciences
medicine
Humans
Caesarean section
Abnormalities
Multiple
Breech Presentation
lcsh:RG1-991
business.industry
Cesarean Section
Uterus
medicine.disease
Patient Care Management
Pregnancy Complications
Urogenital Abnormalities
Settore MED/40 - Ginecologia e Ostetricia
business
Postpartum period
Zdroj: BMC Pregnancy and Childbirth
BMC Pregnancy and Childbirth, Vol 18, Iss 1, Pp 1-5 (2018)
ISSN: 1471-2393
Popis: Background Herlyn–Werner-Wunderlich syndrome (HWWS) is an uncommon congenital anomaly of the female urogenital tract, characterised by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. We reported the difficult pregnancy course complicated by an extremely rare and unique case of this syndrome associated with ectrodactyly, a clinical combination never described in literature. Case presentation A 28- year-old nulliparous woman previously diagnosed for HWWS associated with ectrodactyly of the right foot and with a history of abdominal left hemi-hysterectomy, ipsilateral salpingectomy, vaginal reconstruction when she was an adolescent. She suffered from threats of abortion in the first trimester, recurrent urinary tract infections during all pregnancy. At 33 weeks + 5 days of gestational age, she was hospitalized for premature rupture of the membranes and uterine contractions and a caesarean section was performed because of breech presentation. Postpartum period was complicated by a pelvic abscess resolved with parental antibiotic therapies. Conclusions Our literature review shows an unusual aspect in our case: HWWS is not classically associated with skeletal anomalies. Moreover, the most frequent urogenital side affected is the right, not left side as in this woman. Preterm spontaneous rupture of membranes and fetal abnormal presentation represent frequent complications and probably post-caesarean infections are related to pregnancies in the context of this syndrome.
Databáze: OpenAIRE
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