Autopsy study of pulmonary capillary hemangiomatosis with inflammatory cell infiltration into the myocardium
Autor: | Akimasa Matsuda, Taku Omori, Masaaki Ito, Keiko Ohta-Ogo, Norikazu Yamada, Shiro Nakamori, Kyoko Imanaka-Yoshida, Kaoru Dohi, Yoshito Ogihara |
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Rok vydání: | 2020 |
Předmět: |
Pulmonary and Respiratory Medicine
lcsh:Diseases of the circulatory (Cardiovascular) system Pathology medicine.medical_specialty Case Report Autopsy Pulmonary capillary hemangiomatosis 030204 cardiovascular system & hematology pulmonary capillary hemangiomatosis 03 medical and health sciences 0302 clinical medicine Fibrosis Edema medicine.artery myocardium Medicine Myocytolysis lcsh:RC705-779 Lung business.industry lcsh:Diseases of the respiratory system medicine.disease medicine.anatomical_structure 030228 respiratory system lcsh:RC666-701 Pulmonary artery pathology medicine.symptom business Infiltration (medical) pulmonary artery hypertension |
Zdroj: | Pulmonary Circulation Pulmonary Circulation, Vol 10 (2020) |
ISSN: | 2045-8940 |
Popis: | Pulmonary capillary hemangiomatosis is a rare form of pulmonary artery hypertension; to date, only few descriptions of myocardial pathology in pulmonary capillary hemangiomatosis have been reported in the literature. We report the case of a Japanese female patient who was diagnosed with pulmonary capillary hemangiomatosis combined with acute myocardial inflammation on performing autopsy. She was admitted to our hospital because of acute pneumonia and subsequently suddenly developed severe hypoxemia with breathing difficulty and died 13 days after admission. At autopsy, the histology of the lung was consistent with pulmonary capillary hemangiomatosis. Additionally, a diffuse severe infiltration of inflammatory cells was associated with edema in the myocardium. Myocytolysis was limited and fibrosis was absent. To the best of our knowledge, pulmonary capillary hemangiomatosis with acute myocarditis-like histological findings has been described for the first time through our case. |
Databáze: | OpenAIRE |
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