Replacement of an Implantable Cardioverter-Defibrillator (ICD) with a New Standard Subcutaneous ICD System in a Patient with Jervell and Lange-Nielsen Syndrome
| Autor: | Kenichi Iijima, Tohru Minamino, Nobue Yagihara, Hisanori Haniu, Yuki Hasegawa, Daisuke Izumi, Shuichi Shiraishi, Akinori Sato |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
medicine.medical_specialty
Time Factors medicine.medical_treatment Long QT syndrome 030204 cardiovascular system & hematology QT interval Syncope Electrocardiography 03 medical and health sciences 0302 clinical medicine Internal medicine Humans Medicine Genetic Predisposition to Disease 030212 general & internal medicine Child Device Removal business.industry General Medicine Implantable cardioverter-defibrillator medicine.disease Defibrillators Implantable Pedigree Jervell and Lange-Nielsen syndrome Treatment Outcome Shock (circulatory) KCNQ1 Potassium Channel Retreatment Jervell-Lange Nielsen Syndrome Cardiology Female medicine.symptom Cardiology and Cardiovascular Medicine business Follow-Up Studies |
| Zdroj: | International Heart Journal. 60:1206-1210 |
| ISSN: | 1349-3299 1349-2365 |
| DOI: | 10.1536/ihj.19-076 |
| Popis: | A 7-year-old female suffering from syncope attacks and deafness was genetically diagnosed with Jervell and Lange-Nielsen syndrome (JLNS). A transvenous-designed shock lead and implantable cardioverter-defibrillator (ICD) were atypically implanted subcutaneously, because the patient's body was small. Six years after implantation, we confirmed the patient's eligibility for a subcutaneous ICD (S-ICD) based on electrocardiogram screening. The implanted ICD system was replaced with a new standard S-ICD system. Implantation of the S-ICD may be considered a reliable and safe option in young patients with JLNS, even if their electrocardiograms show remarkable prolongation of the QT interval and T-wave alternans. |
| Databáze: | OpenAIRE |
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