Intimal sarcoma of the pulmonary artery with multiple lung metastases: Long-term survival case
| Autor: | Amalia Palacios-Eito, Elvira Carmona-Asenjo, Alberto L Moreno-Vega, Rosa Ortega-Salas, Sonia García-Cabezas, Simona Espejo-Pérez, Macarena Centeno-Haro |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2017 |
| Předmět: |
medicine.medical_specialty
medicine.medical_treatment Case Report 030204 cardiovascular system & hematology 03 medical and health sciences 0302 clinical medicine Quality of life medicine.artery Medicine Intimal sarcoma of the pulmonary artery Lung business.industry General surgery Metastasectomy Trunk Radiation therapy Treatment medicine.anatomical_structure Oncology Stereotactic body radiation therapy 030220 oncology & carcinogenesis Radiological weapon Pulmonary artery Radiology business Lung metastases Intimal sarcoma |
| Zdroj: | World Journal of Clinical Oncology |
| ISSN: | 2218-4333 |
| Popis: | Pulmonary artery intimal sarcoma (PAIS) is a rare tumor with a very poor prognosis. Clinical and radiological findings usually mimic thromboembolic disease, leading to diagnostic delays. The treatment of choice is surgery, and adjuvant chemotherapy and radiotherapy have limited results. We report the case of a 48-year-old male patient, initially suspected with pulmonary thromboembolism. The angio-CT revealed a filling defect in the pulmonary artery trunk. The patient underwent surgery, resulting in with complete resection of the mass with a diagnosis of PAIS. The tumor progressed rapidly in the lung, requiring surgery of multiple lung metastases. The patient was treated with stereotactic body radiation therapy (SBRT) on two occasions for new pulmonary lesions. In the last followup (4 years after initial diagnosis), the patient was disease-free. In conclusion, SBRT proved to be an alternative treatment to metastasectomy, allowing palliative chemotherapy to be delayed or omitted, which may result in improved quality of life. |
| Databáze: | OpenAIRE |
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