Dermatofibrosarcoma protuberans of the vulva: margins assessment and reconstructive options – a report of two cases
| Autor: | Mariane Campagnari, Glauco Baiocchi, João Pedreira Duprat Neto, Mariana Petaccia de Macedo, Clovis Antonio Lopes Pinto, William Ricardo Camarço, André Sapata Molina, Isabela Werneck da Cunha, Eduardo Bertolli, Eduard Renè Bretchbuhl |
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| Rok vydání: | 2014 |
| Předmět: |
Deep margin
medicine.medical_specialty Reconstructive surgery business.industry Wide local excision medicine.medical_treatment Partial Vulvectomy Case Report Clitoris medicine.disease Vulva Surgery CCPDMA medicine.anatomical_structure Oncology Surgical oncology Dermatofibrosarcoma protuberans medicine DFSP Reconstruction business |
| Zdroj: | World Journal of Surgical Oncology |
| ISSN: | 1477-7819 |
| Popis: | Background Dermatofibrosarcoma Protuberans (DFSP) of the vulva is rare and oncologic surgery with free margins may lead to severe functional damage, requiring multidisciplinary approach regarding resection, margin assessment and reconstruction. Case Report Two cases of DFSP in vulva were treated in a single institution. A 28-year-old patient with an incisional biopsy in the vulvar region revealing DFSP underwent a partial vulvectomy with clitoris preservation. Pathological studies revealed free margins and reconstructive surgery was performed. This patient is disease free in a 40 months follow up. The other, a 57-year-old patient was also referred after an incomplete resection of a DFSP in the vulvar region. A 1-cm margim resection followed by Complete Circumferential and Peripheral Deep Margin Assessment (CCPDMA) was performed. Although the upper lateral margin was positive, it was possible to perform another wide local excision with preservation of the clitoris and primary closure. Conclusion DFSP of the vulva requires an accurate evaluation of margins, resections following oncological principles and reconstruction. Although being a very challenging lesion that usually implies difficult surgical management, if treated in a multidisciplinary environment, with surgical oncologists, experienced dermatopathologists and reconstructive surgeons can achieve good results. Even in difficult cases that presents with large lesions and compromising challenging areas, a complete oncologic resection can be performed minimizing functional damage for the patient. Electronic supplementary material The online version of this article (doi:10.1186/1477-7819-12-399) contains supplementary material, which is available to authorized users. |
| Databáze: | OpenAIRE |
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